Endolymphatic Sac Tumor in von Hippel-Lindau Disease: A Rare Case Report. Biswas, R., Kumari, K., Gupta, S., Haresh, K. P., Halder, A., & Rath, G. K. Journal of Pediatric Neurosciences, 12(3):294–297, 2017.
doi  abstract   bibtex   
Endolymphatic sac tumor (ELST) is a rare papillary neoplasm with locally destructive behavior which can occur sporadically or in association with Von Hippel-Lindau (VHL) disease. We herein present a case of ELST associated with VHL disease in a 14-year-old girl and discuss clinico-radiological, immunohistopathologic findings, and management by staged surgery and postoperative radiotherapy to the residual lesion.
@article{biswas_endolymphatic_2017,
	title = {Endolymphatic {Sac} {Tumor} in von {Hippel}-{Lindau} {Disease}: {A} {Rare} {Case} {Report}},
	volume = {12},
	issn = {1817-1745},
	shorttitle = {Endolymphatic {Sac} {Tumor} in von {Hippel}-{Lindau} {Disease}},
	doi = {10.4103/jpn.JPN_28_17},
	abstract = {Endolymphatic sac tumor (ELST) is a rare papillary neoplasm with locally destructive behavior which can occur sporadically or in association with Von Hippel-Lindau (VHL) disease. We herein present a case of ELST associated with VHL disease in a 14-year-old girl and discuss clinico-radiological, immunohistopathologic findings, and management by staged surgery and postoperative radiotherapy to the residual lesion.},
	language = {eng},
	number = {3},
	journal = {Journal of Pediatric Neurosciences},
	author = {Biswas, Rituparna and Kumari, Kalpana and Gupta, Subhash and Haresh, K. P. and Halder, Anirban and Rath, G. K.},
	year = {2017},
	pmid = {29204213},
	pmcid = {PMC5696675},
	keywords = {Case Study, ELST, Ear, Endolymphatic Sac Tumor},
	pages = {294--297},
}

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